POSSO-OSORIO, Iván; SUA, Luz F.; TOBON, Gabriel J.    FERNANDEZ, Liliana. Pulmonary involvement as the initial manifestation in primary Sjögren's syndrome. []. , 26, 3, pp.209-213.   20--2020. ISSN 0121-8123.  https://doi.org/10.1016/j.rcreu.2018.04.002.

Sjögren's syndrome is a systemic autoimmune disease that mainly affects the exocrine glands, particularly the salivary and the lacrimal glands, but which can also affect other organs such as the skin, and extra-glandular regions such as the heart, kidney, brain, the haematopoietic system and the lung. The case is presented of a patient with primary Sjögren's syndrome, whose first manifestation of the disease was pulmonary hypertension and a non-specific interstitial lung disease, with an absence of sicca symptoms. The patient received treatment with steroids and azathioprine, with an appropriate response. A literature review is also presented on the main pulmonary manifestations in Sjögren's syndrome.

: Primary Sjögren's syndrome; Pulmonary hypertension; Interstitial lung disease.

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