Abstract

RIVAS-GALVEZ, Ronald E. et al. Hedinger syndrome. Rev. Colomb. Cardiol. [online]. 2022, vol.29, n.1, pp.94-99.  Epub Feb 22, 2022. ISSN 0120-5633.  https://doi.org/10.24875/rccar.m22000123.

Cardiac carcinoid tumor involvement (Hedinger’s syndrome) remains a major cause of morbidity and mortality among patients with carcinoid syndrome and metastatic neuroendocrine tumors. The initial imaging study in case of clinical suspicion is the transthoracic echocardiogram, which is important for the early detection of cardiac involvement. Cardiac surgery, in appropriate cases, is the only definitive therapy for carcinoid tumor with cardiac involvement and improves patient symptoms and survival. Treatment is complex and multidisciplinary; cardiac status, hormonal syndrome, and tumor burden are essential to guide the optimal timing of surgery. The case of a young female patient with Hedinger’s syndrome with tricuspid and pulmonary valve involvement, who received surgical treatment and had a successful evolution.

Keywords : Carcinoid tumor; Pulmonary stenosis; Tricuspid valve stenosis.

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