Abstract

RUIZ-GARCIA, Ramiro Gilberto; CHACON-GONZALEZ, Jacobo; BAYLISS, Leo  and  RAMIREZ-BERMUDEZ, Jesús. Neuropsychiatry of Susac Syndrome: a Case Report. rev.colomb.psiquiatr. [online]. 2021, vol.50, n.2, pp.146-151.  Epub Dec 20, 2021. ISSN 0034-7450.

Susac syndrome is a rare clinical condition, possibly mediated by an autoimmune process; the classic triad is composed of retinopathy, decreased hearing acuity and neuropsychiatric symptoms (encephalopathy). There are few cases reported with neuropsychiatric symptoms as the main manifestation. We present a case of Susac syndrome in a 34-year-old female with a predominance of neuropsychiatric symptoms, characterised by partial Klüver-Bucy syndrome, apathy syndrome, pathological laughter and crying, and cognitive dysfunction predominantly affecting attention, which showed a qualitative improvement with the use of immunological therapy. This case report highlights the importance of neuropsychiatric manifestations as clinical presentation in patients with neurological conditions.

Keywords : Apathy; Klüver-Bucy; Pathological laughter and crying; Neuropsychiatric symptoms; Susac síndrome.

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