Abstract

ALCALA-CERRA¹, Gabriel; MOSCOTE-SALAZAR, Luis Rafael; LOZANO-TAGUA, Carlos Fernando  and  SABOGAL-BARRIOS, Rubén. Spontaneous pneumothorax associated with pulmonary fibrosis in a patient with neurofibromatosis type 2. rev.fac.med. [online]. 2010, vol.58, n.2, pp.137-141. ISSN 0120-0011.

Pulmonary involvement in patients with neurofibromatosis has been repetitively reported as a very rare complication in type 1 variety. It is characterized by pulmonary intersticial disease, pulmonary fibrosis and bullaes, the last with high risk of rupture. We described a case of spontaneous pneumothorax in a patient with type 2 neurofibromatosis, as consequence of pulmonary fibrotic changes. To our knowledge this association had not been reported.

Keywords : pneumothorax; pulmonary fibrosis; pulmonary emphysema.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )