Abstract

REQUENA-MENDOZA, Alejandra; CARDENAS-MENDOZA, María Angélica  and  ARGUETA-FIGUEROA, Liliana. Clinical manifestations and complications of Hereditary Sensory and Autonomic Neuropathy Type II. CES odontol. [online]. 2021, vol.34, n.1, pp.108-117.  Epub Feb 17, 2022. ISSN 0120-971X.  https://doi.org/10.21615/cesodon.34.1.10.

The perception of pain is an adaptive response to the presence of harmful and potentially fatal events. Congenital insensitivity to pain, Hereditary Sensory and Autonomic Neuropathy Type II or Morvan syndrome of unknown cause, is a condition in which there is a loss of discrimination of the painful signals, as well as the emotional-affective response. Due to this, the person, that suffering this disorder, does not evade the painful stimuli and, consequently, can inflict damage to himself or herself. Even during the treatment of such lesions can produce serious complications as described in the development of the present clinical case. This syndrome is very rare, hence the importance of publicizing the complications that may occur in order for the medical community to detect this type of patients as soon as possible.

This case report shows the follow-up of a female patient with Hereditary Sensory and Autonomic Neuropathy Type II for ten years. The patient has had several admissions to the hospital, due to infectious processes in the oral cavity that involved multiple dental organs, evolving to osteomyelitis, and for this reason, the mandibulectomy must performed in the patient; even after she underwent several pharmacological treatments.

Despite the efforts to maintain the patient with the best possible quality of life, this case shows that a late diagnosis lead to an unfavorable prognosis and life condition for patients suffering from this genetic anomaly.

Keywords : Pain Insensitivity; Hereditary Sensory and Autonomic Neuropathy Type II; HSAN-Type II; Complications..

        · abstract in Spanish | Portuguese     · text in Spanish     · Spanish ( pdf )