Serviços Personalizados
Journal
Artigo
Indicadores
- Citado por SciELO
- Acessos
Links relacionados
- Citado por Google
- Similares em SciELO
- Similares em Google
Compartilhar
Revista Colombiana de Cardiología
versão impressa ISSN 0120-5633
Resumo
MORA, Guillermo; LAVERDE, Ligia P e PALACIO, Ana C. Progressive familial atrio-ventricular block type I: clinical description of a family. Rev. Colomb. Cardiol. [online]. 2011, vol.18, n.5, pp.279-281. ISSN 0120-5633.
We present the case of a family with atrio-ventricular block that involves several generations, with dominant autosomal mendelian inheritance that progressively affects the cardiac conduction system leading to syncope and sudden death in early life. This entity corresponds to progressive familial atrio-ventricular block type I, described mainly in South Africa . Treatment with permanent pacemaker therapy was successful.
Palavras-chave : familial heart block; progressive cardiac conduction defect; hereditary bundle branch block.