Abstract

PACHAJOA, Harry. Cantrell's pentalogy in the first twin from a monozygotic twin pregnancy: a case presentation and literature review. Rev Colomb Obstet Ginecol [online]. 2011, vol.62, n.1, pp.94-97. ISSN 0034-7434.

Introduction: Cantrell's pentalogy (CP) consists of five anomalies: upper abdominal wall defects, lower sternal defects, anterior diaphragmatic defects, diaphragmatic pericardial defects and abnormalities of the heart. Around 250 cases have been reported; only 6 have involved twins and 4 of these have described discordance of such anomaly. Objective: presenting a case of twin pregnancy-associated CP and literature review regarding such association, emphasizing prenatal diagnosis and etiology. Materials and methods: a case of Cantrell’s pentalogy is presented which only affected the first twin from a monozygotic twin pregnancy. Information was sought in SciELO and PubMed databases, using the following MeSH terminology "Pentalogy of Cantrell", "Twin" and "Pentalogía de Cantrell" and "gemelar" in Spanish. Conclusion: CP may be ecographically suspected by ectopia cordis and thoracoabdominal defects. The presentation of a case in twin pregnancy is an extremely rare association.

Keywords : Cantrell's pentalogy; monozygotic twin pregnancy; onphalocele.

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