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Revista Colombiana de Cardiología
versión impresa ISSN 0120-5633
Resumen
CONTRERAS Z, Eduardo; GOMEZ M, Juan E y ZULUAGA M, Sandra X. Long QT syndrome. Rev. Col. Cardiol. [online]. 2008, vol.15, n.1, pp.12-17. ISSN 0120-5633.
Long QT syndrome is a disease characterized by the electrocardiographic alteration in ventricular repolarization manifested by prolonged QT interval, secondary to prolonged ventricular repolarization. This makes these patients more vulnerable to very fast ventricular arrhythmias such as torsade des pointes or ventricular fibrillation. This syndrome is generally observed in young people and is associated with sudden death. It may appear as part of congenital LQTS (Jervell and Lange-Nielsen and Romano-Ward), or may be secondarily acquired due to metabolic or toxic alterations or to other physiopathologic factors.
Palabras clave : long QT syndrome; sudden death; repolarization disorders; arrhythmias.