SciELO - Scientific Electronic Library Online

 
vol.24 issue4Pulmonary thromboembolism associated to superior vena cava syndrome thrombotic originOpen-heart mapping and radiofrequency ablation: a case of refractory ventricular tachycardia in Ebstein’s anomaly author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand

Article

Indicators

Related links

  • On index processCited by Google
  • Have no similar articlesSimilars in SciELO
  • On index processSimilars in Google

Share


Revista Colombiana de Cardiología

Print version ISSN 0120-5633

Abstract

RODRIGUEZ-GONZALEZ, María Juliana; TORRES, Ángela M.  and  ECHEVERRIA, Luis E.. Endomyocardial fibrosis. Rev. Colomb. Cardiol. [online]. 2017, vol.24, n.4, pp.407-407. ISSN 0120-5633.  http://dx.doi.org/10.1016/j.rccar.2016.07.006.

Cardiomyopathies are intrinsic conditions of the cardiac muscle. They present differential phenotypes that determine their classification. These are: dilated, hypertrophic, restrictive, arrhythmogenic right ventricular and unclassified. Restrictive cardiomyopathies are characterised by larger than normal ventricles with normal or slightly enlarged thickness of the walls, rigid walls, severe diastolic dysfunction and restrictive filling with high pressures.

One of the most common restrictive cardiomyopathies is endomyocardial fibrosis, which is endemic to some tropical areas, especially Africa (low income countries), but there are few reports of its occurrence in our environment. Its aetiology is unknown, but there are several mechanisms that have been involved in its pathophysiology. Its diagnosis is based in imaging studies (transthoracic echocardiogram, cardiac nuclear magnetic resonance). Prognosis is very poor, and it is usually diagnoses in the latest stages of the disease. The case of a female, average adult patient that debuted with restrictive cardiomyopathy with a final diagnosis of endomyocardial fibrosis is described.

Keywords : Restrictive cardiomyopathy; Endomyocardial fibrosis; Nuclear magnetic resonance.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )