Abstract

VARGAS-VERGARA, Diana et al. Description of two cases of ALCAPA syndrome. Rev. Colomb. Cardiol. [online]. 2021, vol.28, n.1, pp.98-101.  Epub Mar 19, 2021. ISSN 0120-5633.  https://doi.org/10.24875/rccar.m21000016.

The anomalous origin of the left coronary artery from the pulmonary artery or its acronym ALCAPA syndrome (Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery), also known as Blande-Whitee-Garland syndrome, is a rare congenital heart disease. However, one of the most common causes of heart failure, ischemia and myocardial infarction in children, which in the absence of treatment, reaches a mortality rate of 35 to 85% in the first year of life. There are two types of ALCAPA syndrome, that occurs in infants and adults. The presentation of the second type is rare and can manifest as myocardial infarction, left ventricular dysfunction and mitral insufficiency, or silent ischemia that could lead to sudden death. We present the case of a 30-year-old patient with dilated cardiomyopathy and severe ventricular dysfunction, secondary to the ALCAPA syndrome, another case of a 61-year-old patient with chest pain where the mentioned syndrome was documented.

Keywords : ALCAPA syndrome; Ventricular dysfunction; Bland-White-Garland syndrome.

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