Abstract

MARTINEZ-MONTALVO, Carlos M. et al. Sarcoma of the pulmonary vein. Rev. Colomb. Cardiol. [online]. 2022, vol.29, n.3, pp.373-377.  Epub Sep 01, 2022. ISSN 0120-5633.  https://doi.org/10.24875/rccar.m22000166.

Sarcomas are primary neoplasms, whose location is rare in large vessels and in the pulmonary veins is exceptional. The two most frequent types in the pulmonary vein are leiomyosarcoma and fibrosarcoma, distribution around 4 and 5 decades of life, with a prognosis of 23 months and 60% metastasis at the time of diagnosis. The clinical presentation is nonspecific simulating situations such as pulmonary embolism, decompensated heart failure and mass in the left atrium. Different tools are available for its diagnosis, like echocardiography, computed tomography, coronary angiography, magnetic resonance imaging and PET CT. Treatment includes radical surgical resection, adjuvant therapy with chemotherapy, and radiation therapy, even heart transplantation in selected cases. It is presented the case of a patient with an initial diagnosis of pulmonary embolism, with an episode of pulmonary edema secondary to a mass in the left atrium, extension of a sarcoma of the right pulmonary vein, with a fatal outcome. We contributed to the literature with the case and review of theme.

Keywords : Pulmonary vein sarcoma; Pulmonary embolism; Primary cardiac tumor.

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