Abstract

ALEMAN-INIGUEZ, Juan Miguel; ALEMAN-INIGUEZ, Pedro José  and  GUILLEN, Fernando. Rapidly progressive dementia in sporadic prion disease: report of unprecedented event in Ecuador and update. Acta Neurol Colomb. [online]. 2016, vol.32, n.2, pp.169-178. ISSN 0120-8748.

Sporadic prion disease is an unusual condition in Latin American populations. The etiology is genetic alteration that causes an aberrant misfolded protein that accumulates in various encephalic structures, generating rapid dementia and subsequently variables neurological deficits. The aim is to present a particular multisystem impairment related to the sporadic variant of Creutzfeldt-Jakob disease that this fact makes it a diagnostic challenge.

Keywords : Creutzfeldt Jakob; dementia; rapidly progression dementya.

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