Abstract

ROMERO HERNANDEZ, Camilo Andrés  and  RAMIREZ RODRIGUEZ, Natalia. Miescher-Melkersson-Rosenthal Syndrome: Three cases reports and literature review. Acta Neurol Colomb. [online]. 2021, vol.37, n.2, pp.75-79.  Epub July 06, 2021. ISSN 0120-8748.  https://doi.org/10.22379/24224022370.

Miescher-Melkerson-Rosenthal syndrome is an uncommon clinical condition characterized by episodic orofacial oedema, recurrent peripheral facial paralysis, geographic tongue (lingua plicata) and granulomas in skin or labial biopsy. It is reported more frequently in women, and its incidence is probably underestimated due to lack of knowledge of the syndrome, incomplete clinical presentation and the plethora of differential diagnosis. It should be considered in patients with at least two of the four mentioned characteristics. Its treatment, with oral steroids, is directed at the episodes of orofacial oedema and/or the facial paralysis. We described three cases of the syndrome seen at the Fundacion Cardioinfantil's neurology service and present a short review of the literature.

Keywords : angioedema; facial paralysis; fissured tongue; Melkersson-Rosenthal syndrome (MeSH).

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