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Revista colombiana de Gastroenterología

versión impresa ISSN 0120-9957versión On-line ISSN 2500-7440

Resumen

Poliposis adenomatosa familiar atenuada: Entidad controvertida. Rev Col Gastroenterol [online]. 2004, vol.19, n.3, pp.223-227. ISSN 0120-9957.

Attenuated Familial Adenomatous Polyposis is an entity poorly understood for medical groups, is a variant of Familial Adenomatous Polyposis, characterized by fewer colorectal polyps, begin of polyps and cancer in later age than classic variant, and predilection for proximal ubication. Colonoscopy shows multiple flat adenomas, and histopathology is characterized by tubular adenomas with displasia in high percentage. Diagnosis is difficult for abscence of specific finding or genetic proube, must be based in clinical and endoscopy findings, and treatment varies from polypectomy to total colectomy. In this review we present the history, etiology, clinical presentation, diagnosis, and treatment of this pathology, and the experience with this pathology in our sevice.

Palabras clave : Attenuated polyposis; familial adenomatous polyposis; polyposis syndromes; polypectomy.

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