Abstract

RESTREPO, Mauricio et al. Churg-Strauss syndrome: a case with unusual manifestations. Rev.Colomb.Reumatol. [online]. 2009, vol.16, n.1, pp.112-119. ISSN 0121-8123.

Churg-Strauss syndrome, a necrotizing systemic vasculitis which involves the small and (more rarely) the medium-sized vessels, is a primary vasculitis strongly associated with antineutrophil cytoplasm antibodies (ANCA). It is characterized by the presence of asthma, eosinophilia and extravascular eosinophilic granulomas. Herein, we report a 36-year-old woman with a history of late onset asthma and allergic rhinitis who developed central nervous system involvement, peripheral neuropathy, leukocytoclastic vasculitis and eosinophilia. Interestingly, unusual clinical manifestations of Churg-Strauss syndrome such as mesenteric microaneurysms and jaw claudication were present in this particular patient. A brief review of the literature of Churg-Strauss syndrome is presented.

Keywords : vasculitis; Churg-Strauss syndrome; ANCA; mesenteric microaneurysms.

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