Resumo

HERNANDEZ-ACOSTA, Reinei; BASTIDAS-GOYES, Alirio  e  HERNANDEZ-RINCON, Erwin. Granulomatosis with polyangiitis: A case report of early systemic fulminant presentation. Rev.Colomb.Reumatol. [online]. 2022, vol.29, n.3, pp.225-230.  Epub 28-Ago-2023. ISSN 0121-8123.  https://doi.org/10.1016/j.rcreu.2020.08.006.

Granulomatosis with polyangiitis is a systemic vasculitis that affects medium and small vessels, with high expression of anti-neutrophil cytoplasmic autoantibody. A case is pre sented on a patient with an initial compromise of the lower airway, who did not respond to management, required intensive care unit management, and died due to severe diffuse alveolar hemorrhage. His definitive diagnosis was established with a clinical autopsy. Gran-ulomatosis with polyangiitis is a disease with different ways of presentation, and can have fatal outcomes if it is not diagnosed early.

Palavras-chave : Granulomatosis with polyangiitis; ANCA-associated vasculitis; Mortality.

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