Abstract

SUAREZ TERAN, María José; CACERES FERNANDEZ, Pablo Marcelo; ARMIJOS VILLACIS, Christian Augusto  and  TORRES HERRERA, Gabriela Alexandra. IgG4-related disease associated with immune thrombocytopenia: A clinical case report. Rev.Colomb.Reumatol. [online]. 2022, vol.29, n.4, pp.384-389.  Epub Aug 18, 2023. ISSN 0121-8123.  https://doi.org/10.1016/j.rcreu.2021.02.001.

Autoimmune pancreatitis is a characteristic manifestation of the spectrum of the disease related to IgG4, a rare autoimmune disorder that presents clinically with obstructive jaundice due to the infiltration of plasma cells and fibrosis in the pancreas. There may be other symptoms in case of involvement of other organs, and in very rare cases there is hematological involvement. We present the case of an adult man with signs of cholestasis secondary to type I autoimmune pancreatitis, with involvement of other organs and associated with thrombocytopenia that improved with systemic corticosteroid-based immunosuppressive treatment, after which the patient showed favorable clinical and analytical evolution over time.

Keywords : Autoimmune pancreatitis; Immunoglobulin G4-related disease; Thrombocytopenia.

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