Abstract

ARIAS, Sara; GOMEZ, Mariana  and  CELIS, Luis Gustavo. Susac Syndrome: Case Report. Nova [online]. 2015, vol.13, n.24, pp.101-106. ISSN 1794-2470.

The presented patient is a female of 23 years of age, with left-sided temporal headache, of the oppressive kind, associated with ataxia, disoriented in space and time, and mental slowing. The initial approach was to work toward a possible multiple sclerosis; then, the clinical and paraclinical tests arose the suspicion of an acute disseminated encephalomyelitis which was treated with methylprednisolone pulse and given discharge. Within a month, the patient returns for exacerbation of neurological symptoms given by loss of strength in upper and lower limbs, dysarthria, wetting, drowsiness; so the differential diagnosis that was given was Devic's disease, and as she was not responding properly to corticosteroids, it is decided to try with plasmapheresis. Finally the patient was focused with a possible diagnosis of Susac Syndrome with an arteriography paraclinical retinal and auditory evoked potentials.

Keywords : Multiple Sclerosis; Devic's disease; Susac syndrome; acute encephalomyelitis; ataxia; hyporeflexia; alopsiquia; mutism; bradypsychia.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )