<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0120-5633</journal-id>
<journal-title><![CDATA[Revista Colombiana de Cardiología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Colomb. Cardiol.]]></abbrev-journal-title>
<issn>0120-5633</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Colombiana de Cardiologia. Oficina de Publicaciones]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0120-56332017000100040</article-id>
<article-id pub-id-type="doi">10.1016/j.rccar.2016.06.016</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Situs inversus totalis: revisión de tema con aproximación a la Genética y reporte de casos]]></article-title>
<article-title xml:lang="en"><![CDATA[Situs inversus totalis , topic review approach to Genetics and case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Reales]]></surname>
<given-names><![CDATA[Vicente de Jesús Aljure]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gallego]]></surname>
<given-names><![CDATA[Gloria Camila Álvarez]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Espitia]]></surname>
<given-names><![CDATA[Nasly Consuelo Ávila]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Coley]]></surname>
<given-names><![CDATA[Alexandra Arrieta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Suárez]]></surname>
<given-names><![CDATA[Orlando Germany Ángel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Nacional de Colombia  ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital San Rafael  ]]></institution>
<addr-line><![CDATA[Tunja ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad Pedagógica y Tecnológica de Colombia  ]]></institution>
<addr-line><![CDATA[Tunja ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Universidad Nacional de Colombia  ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>02</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>02</month>
<year>2017</year>
</pub-date>
<volume>24</volume>
<numero>1</numero>
<fpage>40</fpage>
<lpage>47</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_arttext&amp;pid=S0120-56332017000100040&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_abstract&amp;pid=S0120-56332017000100040&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_pdf&amp;pid=S0120-56332017000100040&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Objetivo:  Efectuar una revisión actualizada del situs inversus totalis y presentar casos clínicos.  Métodos:  Se hizo una revisión de las principales bases de datos y se incluyeron los estudios más relevantes correspondientes a 20 a&#732;nos previos, en espa&#732;nol e inglés, en todos los grupos etáreos y étnicos, incluidos: metaanálisis, revisiones sistemáticas, ensayos clínicos, estudios de cohorte y casos clínicos relevantes. Se consultaron bases de datos como EBSCO, Medline, PubMed y SciELO entre otras, para obtener información actualizada. Los términos de búsqueda fueron situs inversus, totalis.  Resultados:  El situs inversus totalis es una variante anatómica poco frecuente que involucra estructuras toraco-abdominales, hace parte de otras variantes de situs, tiene un patrón de herencia poligénico, sin una relación directa establecida; es además una entidad asintomática, reconocida desde tiempos antiguos.  Conclusiones:  Aunque es una patología de baja incidencia en la población, y un hallazgo incidental, es importante reconocerla como una variante anatómica que puede cursar con patologías concomitantes. A pesar de que existen estudios, se requieren otros con alta significancia estadística. Se encuentra relación de los casos con la información de la literatura que concluyen un estudio acertado.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objective:  To conduct an updated review of situs inversus totalis and present clinical cases.  Methods:  A review of the main databases was conducted, and the most relevant studies over the last 20 years were included, both in Spanish and English, in all age and ethnic groups,  including:  meta-analysis, systematic reviews, clinical trials, cohort studies and relevant clinical cases. Databases such as EBSCO, Medline, PubMed and SciELO were consulted among others to obtain updated information. Search terms were &#8216;&#8216;situs inversus&#8217;&#8217;, &#8216;&#8216;totalis&#8217;&#8217;.  Results:  Situs inversus totalis is a rare anatomical variant that involves thoracoabdominal structures, takes part in other situs variants, has a polygenic inheritance pattern, without a direct established relationship; is also an asymptomatic entity, recognised since ancient times.  Conclusion:  Despite being a condition with a low incidence in the population and having an incidental finding, it is important to recognise it as an anatomical variant that can coexist with concomitant diseases. Although studies exist, more are required with a higher statistical significance. A relationship is found between the cases with the information found in the literature, which leads to a strong research&lt;/org&gt;.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Situs inversus]]></kwd>
<kwd lng="es"><![CDATA[Anomalías congénitas]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Kartagener]]></kwd>
<kwd lng="es"><![CDATA[Genética]]></kwd>
<kwd lng="en"><![CDATA[Situs inversus]]></kwd>
<kwd lng="en"><![CDATA[Congenital anomalies]]></kwd>
<kwd lng="en"><![CDATA[Kartagener syndrome]]></kwd>
<kwd lng="en"><![CDATA[Genetics]]></kwd>
</kwd-group>
</article-meta>
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