<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0120-5633</journal-id>
<journal-title><![CDATA[Revista Colombiana de Cardiología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Colomb. Cardiol.]]></abbrev-journal-title>
<issn>0120-5633</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Colombiana de Cardiologia. Oficina de Publicaciones]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0120-56332022000200209</article-id>
<article-id pub-id-type="doi">10.24875/rccar.m22000148</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Scimitar syndrome with late presentation]]></article-title>
<article-title xml:lang="es"><![CDATA[El síndrome de la cimitarra con presentación tardía]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García-Henao]]></surname>
<given-names><![CDATA[Laura María]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Duque]]></surname>
<given-names><![CDATA[Santiago A.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Erazo-Criollo]]></surname>
<given-names><![CDATA[Héctor M.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Caldas Facultad de Ciencias para la Salud ]]></institution>
<addr-line><![CDATA[Manizales ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Universitario de Caldas SES Hospital Universitario de Caldas SES ]]></institution>
<addr-line><![CDATA[Manizales ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<volume>29</volume>
<numero>2</numero>
<fpage>209</fpage>
<lpage>214</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_arttext&amp;pid=S0120-56332022000200209&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_abstract&amp;pid=S0120-56332022000200209&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_pdf&amp;pid=S0120-56332022000200209&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction: Scimitar syndrome is a congenital malformation with an incidence of 1-3 per 100,000 live births, consisting of abnormal drainage of the right pulmonary veins. The age of diagnosis varies according to the severity of the pathology, which depends on the degree of cardiac and pulmonary malformation. The case of a patient with a late diagnosis of the syndrome due to a silent course is reported despite severe anatomical alterations.  Clinical Case: A 76-year-old female was admitted due to a 6-month clinical picture of progressive dyspnea to minimal efforts. A transthoracic echocardiogram was performed showing severe pulmonary hypertension of 96 mmHg with abnormal communication between the right pulmonary veins and the inferior vena cava, confirmed by CT angiography.  Discussion: The late clinical course in relation to severe anatomical malformations has not been described in the scientific literature due to its high mortality in childhood.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Introducción: El síndrome de la cimitarra es una malformación congénita con una incidencia de 1 a 3 por cada 100,000 nacidos vivos, que consiste en un drenaje anormal de las venas pulmonares derechas. La edad en el momento del diagnóstico varía según la severidad de la patología, la cual depende del grado de malformación cardíaca y pulmonar. Se reporta el caso de una paciente con diagnóstico tardío del síndrome dado por un curso silencioso a pesar de tener alteraciones anatómicas severas.  Caso clínico: mujer de 76 años de edad quien se hospitaliza por un cuadro clínico de seis meses de evolución consistente en disnea progresiva de mínimos esfuerzos. Se le practica un ecocardiograma transtorácico evidenciando hipertensión pulmonar severa de 96 mmHG con una comunicación anormal entre las venas pulmonares derechas y la vena cava inferior, confirmada por angiografía por TC.  Discusión: El curso clínico tardío con relación a las malformaciones anatómicas severas no se ha descrito en la literatura científica dada su alta mortalidad en la infancia.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Scimitar syndrome]]></kwd>
<kwd lng="en"><![CDATA[Pulmonary hypertension]]></kwd>
<kwd lng="en"><![CDATA[Heart septal defects]]></kwd>
<kwd lng="en"><![CDATA[Atrial]]></kwd>
<kwd lng="en"><![CDATA[Heart diseases]]></kwd>
<kwd lng="en"><![CDATA[Lung diseases]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de la cimitarra]]></kwd>
<kwd lng="es"><![CDATA[Hipertensión Pulmonar]]></kwd>
<kwd lng="es"><![CDATA[Defectos Septales Cardíacos]]></kwd>
<kwd lng="es"><![CDATA[Atrial]]></kwd>
<kwd lng="es"><![CDATA[Enfermedades Cardíacas]]></kwd>
</kwd-group>
</article-meta>
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