<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0121-0793</journal-id>
<journal-title><![CDATA[Iatreia]]></journal-title>
<abbrev-journal-title><![CDATA[Iatreia]]></abbrev-journal-title>
<issn>0121-0793</issn>
<publisher>
<publisher-name><![CDATA[Universidad de Antioquia]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0121-07932017000100081</article-id>
<article-id pub-id-type="doi">10.17533/udea.iatreia.v30n1a08</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Kinsbourne: reporte de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Kinsbourne syndrome: Report of a case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Síndrome de Kinsbourne: reporte de um caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Paredes-Ebratt]]></surname>
<given-names><![CDATA[Ángela María]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Espinosa-García]]></surname>
<given-names><![CDATA[Eugenia Teresa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Militar Nueva Granada  ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Militar Nueva Granada  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<volume>30</volume>
<numero>1</numero>
<fpage>81</fpage>
<lpage>85</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_arttext&amp;pid=S0121-07932017000100081&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_abstract&amp;pid=S0121-07932017000100081&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_pdf&amp;pid=S0121-07932017000100081&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El síndrome de Kinsbourne, conocido también como &#8220;síndrome de opsoclonus-mioclonus&#8221; o &#8220;síndrome de los ojos danzantes&#8221;, es una enfermedad rara caracterizada por movimientos oculares rápidos, irregulares, multidireccionales (opsoclonus), movimientos mioclónicos en tronco, cara y/o extremidades y ataxia; se presenta entre los 6 y 36 meses de edad. Su etiología puede ser paraneoplásica (neuroblastoma), no paraneoplásica (infecciosa) o idiopática. Independientemente de la causa, se han utilizado inmunosupresores para reducir la formación de anticuerpos posiblemente involucrados en su fisiopatología. Presentamos el caso de una niña lactante de 21 meses con este síndrome secundario a un cuadro respiratorio viral. Tuvo ataxia, opsoclonus, mioclonías de miembros superiores, irritabilidad y alteración en el patrón de sueño. Se descartó el diagnóstico de neuroblastoma. El tratamiento inicial se hizo con pulsos de metilprednisolona seguida de prednisolona oral. Sus síntomas desaparecieron progresivamente y recuperó la marcha; actualmente está asintomática y sin secuelas. En estos pacientes se debe descartar siempre un síndrome paraneoplásico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[SUMMARY Kinsbourne syndrome, also known as &#8220;Opsoclonus-myoclonus syndrome&#8221; or &#8220;Dancing eyes syndrome&#8221; is a rare condition characterized by rapid, irregular, multi-directional eye movements (opsoclonus), myoclonic movements in the trunk, face and/or limbs and ataxia. It occurs in children aged between 6 and 36 months. Its etiology may be paraneoplasic (neuroblastoma), non-paraneoplasic (infectious processes) or idiopathic. Regardless of its etiology, immunosuppressive drugs have been used in order to reduce the formation of antibodies possibly involved in the pathophysiology. We report the case of a 21 month-old girl with this syndrome secondary to an infectious respiratory illness. She had ataxia, opsoclonus, upper limbs myoclonus, irritability and altered sleep pattern. Neuroblastoma was ruled out. Initial management was done with methylprednisolone pulses, followed by oral prednisolone. She had progressive clinical improvement, and is currently asymptomatic with no sequelae. In these patients a paraneoplasic syndrome should always be ruled out.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[RESUMO A síndrome de Kinsbourne, conhecida também como &#8220;síndrome de opsoclonus-mioclonus&#8221; a &#8220;síndrome dos olhos dançantes&#8221;, é uma doença rara caracterizada por movimentos oculares rápidos, irregulares, multidirecionais (opsoclonus), movimentos mioclônicos em tronco, cara e/ou extremidades e ataxia; se apresenta entre os 6 e 36 meses de idade. Sua etiologia pode ser paraneoplásica (neuroblastoma), não paraneoplásica (infecciosa) ou idiopática. Independentemente da causa, se há utilizado imunossupressores para reduzir a formação de anticorpos possivelmente envolvidos em sua fisiopatologia. Apresentamos o caso de uma criança lactante de 21 meses com esta síndrome secundária a um quadro respiratório viral. Teve ataxia, opsoclonus, mioclonias de membros superiores, irritabilidade e alteração no padrão de sono. Se descartou o diagnóstico de neuroblastoma. O tratamento inicial se fez com pulsos de metilprednisolona seguida de prednisolona oral. Seus sintomas desapareceram progressivamente e recuperou a marcha; atualmente está assintomática e sem sequelas. Nestes pacientes se deve descartar sempre uma síndrome paraneoplásico.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Ataxia]]></kwd>
<kwd lng="es"><![CDATA[Infección]]></kwd>
<kwd lng="es"><![CDATA[Mioclonus]]></kwd>
<kwd lng="es"><![CDATA[Opsoclonus]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Kinsbourne]]></kwd>
<kwd lng="en"><![CDATA[Ataxia]]></kwd>
<kwd lng="en"><![CDATA[Infection]]></kwd>
<kwd lng="en"><![CDATA[Kinsbourne syndrome]]></kwd>
<kwd lng="en"><![CDATA[Myoclonus]]></kwd>
<kwd lng="en"><![CDATA[Opsoclonus]]></kwd>
<kwd lng="pt"><![CDATA[Ataxia]]></kwd>
<kwd lng="pt"><![CDATA[Infecção]]></kwd>
<kwd lng="pt"><![CDATA[Mioclonus]]></kwd>
<kwd lng="pt"><![CDATA[Opsoclonus]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome de Kinsbourne]]></kwd>
</kwd-group>
</article-meta>
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