<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0120-5552</journal-id>
<journal-title><![CDATA[Revista Salud Uninorte]]></journal-title>
<abbrev-journal-title><![CDATA[Salud, Barranquilla]]></abbrev-journal-title>
<issn>0120-5552</issn>
<publisher>
<publisher-name><![CDATA[Fundación Universidad del Norte, División de Ciencias de la]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0120-55522017000100007</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Enfermedades raras y catastróficas en un hospital del norte peruano: Características y factores asociados a la mortalidad]]></article-title>
<article-title xml:lang="en"><![CDATA[Rare and catastrophic illness in a hospital of northern Peru: Characteristics and factors associated with mortality]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Valladares-Garrido]]></surname>
<given-names><![CDATA[Mario J.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Valladares-Garrido]]></surname>
<given-names><![CDATA[Danai]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bazán-Ruiz]]></surname>
<given-names><![CDATA[Susy]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mejia]]></surname>
<given-names><![CDATA[Christian R.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Peruana Cayetano Heredia  ]]></institution>
<addr-line><![CDATA[Lima ]]></addr-line>
<country>Peru</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Sociedad Científica de Estudiantes de Medicina de la UCV-Piura (SOCIEM-UCV)  ]]></institution>
<addr-line><![CDATA[Piura ]]></addr-line>
<country>Perú</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad Nacional de Piura  ]]></institution>
<addr-line><![CDATA[Piura ]]></addr-line>
<country>Peru</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Universidad Privada Antenor Orrego  ]]></institution>
<addr-line><![CDATA[Lima ]]></addr-line>
<country>Peru</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2017</year>
</pub-date>
<volume>33</volume>
<numero>1</numero>
<fpage>7</fpage>
<lpage>15</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_arttext&amp;pid=S0120-55522017000100007&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_abstract&amp;pid=S0120-55522017000100007&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_pdf&amp;pid=S0120-55522017000100007&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Objetivos: El objetivo fue determinar las características y los factores asociados a la mortalidad en los pacientes atendidos por enfermedades raras (ER) y catastróficas (EC) en un hospital de la seguridad social del norte peruano.  Materiales y métodos: Estudio transversal analítico, se utilizaron datos reportados de pacientes atendidos en un hospital del norte del Perú durante el año 2013. Se caracterizó a los pacientes, las enfermedades y se obtuvieron datos estadísticos de asociación.  Resultados: De los 2316 pacientes, 2135 (92%) tuvieron EC y 181 (8%) ER. La enfermedad más común fue la insuficiencia renal crónica inespecífica (43%), pero la deficiencia hereditaria del factor VIII fue la que generó mayor gasto total (más de 850 426,35 &#8364;) y por cada paciente (2115,49 &#8364;). En el análisis multivariado se encontró asociación con la mortalidad al sexo femenino (p&lt;0,001, RPa: 1,76, IC95%:1,67-1,86), la edad (p&lt;0,001, RPa: 1,02, IC95%:1,01-1,03) y la cantidad de días hospitalizados (p&lt;0,001, RPa: 1,08, IC95%:1,07-1,09), ajustando por el tipo de enfermedad.  Conclusión: Existen características económicas y factores asociados a la mortalidad en los pacientes atendidos en nuestro medio, por lo que deberían realizarse más investigaciones para conocer mejor sobre este grupo, ya que generalmente se encuentra desatendido.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objective: The objective was to determine the characteristics and factors associated with mortality in patients treated for rare diseases (ER) and catastrophic diseases (EC) in a public hospital in northern Peru.  Materials and methods: An analytical cross-sectional study. Data are reported of patients treated in a hospital in northern Peru during 2013. Patients and the disease were characterized and statistical data was obtained.  Results: Of the 2316 patients, 2135 (92%) had EC and 181 (8%) ER. The most common disease was nonspecific chronic renal failure (43%), but the hereditary factor VIII deficiency generated higher total spending (more than 850 426,35 &#8364;) and higher spending per patient (2115,49 &#8364;). The multivariate analysis found an association between mortality and gender (female) (p&lt;0,001, RPa: 1,76, 95% CI:1,67 to1,86), age (p&lt;0,001, RPa: 1,02, 95% CI:1,01 to 1,03) and the number of hospitalized days (p&lt;0,001, RPa: 1,08, 95% CI:1,07 to 1,09).  Conclusions: There are economic characteristics and factors associated with mortality in patients in our region. Additional research should be conducted to learn more about this group of patients, which are already generally neglected.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Enfermedad rara]]></kwd>
<kwd lng="es"><![CDATA[enfermedad olvidada]]></kwd>
<kwd lng="es"><![CDATA[enfermedad catastrófica]]></kwd>
<kwd lng="es"><![CDATA[costos]]></kwd>
<kwd lng="es"><![CDATA[Perú (Fuente: DeCS BIREME)]]></kwd>
<kwd lng="en"><![CDATA[Rare Disease Forgotten Disease]]></kwd>
<kwd lng="en"><![CDATA[Catastrophic Illnesses Costs]]></kwd>
<kwd lng="en"><![CDATA[Peru (Source: MeSH NLM)]]></kwd>
</kwd-group>
</article-meta>
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