<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2500-5006</journal-id>
<journal-title><![CDATA[Revista Colombiana de Nefrología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. colom. nefrol.]]></abbrev-journal-title>
<issn>2500-5006</issn>
<publisher>
<publisher-name><![CDATA[Asociación Colombiana de Nefrología e Hipertensión Arterial]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2500-50062021000200703</article-id>
<article-id pub-id-type="doi">10.22265/acnef.8.2.516</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Crisis renal esclerodérmica]]></article-title>
<article-title xml:lang="en"><![CDATA[Sclerodermal kidney crisis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pedroza Pallares]]></surname>
<given-names><![CDATA[Álvaro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Castiglioni]]></surname>
<given-names><![CDATA[Teresa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bouza]]></surname>
<given-names><![CDATA[Gabriel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Sanatorio de los Arcos Servicio de Medicina Interna ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro de Patología Servicio Anatomía Patológica ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Sanatorio de los Arcos Jefe de Servicio Medicina Interna ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Argentina</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<volume>8</volume>
<numero>2</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_arttext&amp;pid=S2500-50062021000200703&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_abstract&amp;pid=S2500-50062021000200703&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.co/scielo.php?script=sci_pdf&amp;pid=S2500-50062021000200703&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La esclerosis sistémica (ES) es una enfermedad inmuno-mediada, caracterizada por la presencia de fibrosis e inflamación tisular que conlleva cambios degenerativos vasculares de la piel y órganos internos tales como pulmones, corazón, tracto gastrointestinal y riñones. La crisis renal esclerodérmica (CRE), manifestación grave en el riñón, se caracteriza por: hipertensión maligna de inicio súbito, asociada al aumento de la actividad de renina plasmática. Hay una variante clínica que cursa con normotensión, la cual es de peor pronóstico; Insuficiencia Renal Aguda (IRA); y microangiopatía trombótica. A continuación, vamos a relatar la presentación de un caso de CRE en un paciente de 60 años, sexo femenino, quien ingresó al Sanatorio de los Arcos en Buenos Aires, Capital Federal (Argentina) con un cuadro caracterizado por una crisis hipertensiva tipo emergencia, caída de filtrado glomerular severa, micro hematuria y proteinuria. Recibió tratamiento médico, pero por persistencia de signos y síntomas, se decidió realizar una punción biopsia renal, la cual confirmó el diagnóstico. La hematuria microscópica y los cilindros son infrecuentes.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Systemic sclerosis (SS) is characterized by the thickening and hardening of the skin (from the Greek "sclero"); it has forms of limited and diffuse manifestation. It is chronic in pattern and manifests as vascular dysfunction and severe systemic connective fibrosis. Scleroderma renal crisis (CRE) is a severe manifestation in the kidney characterized by malignant hypertension of sudden onset associated with increased plasma renin activity. There is a clinical variant with normotension which has a worse prognosis called Acute Renal Failure (ARF), and thrombotic microangiopathy. Microscopic hematuria and casts are uncommon. We report a case of scleroderma renal crisis (CRE) in a 60-year-old female patient who entered the Sanatorio de los Arcos in Buenos Aires, Capital Federal (Argentina) with severe arterial hypertension, severe glomerular filtration drop, microhematuria and proteinuria. She received medical treatment; nevertheless, it was decided to perform a renal biopsy puncture due to the persistence of signs and symptoms, which confirmed the diagnosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Insuficiencia renal aguda]]></kwd>
<kwd lng="es"><![CDATA[esclerosis sistémica]]></kwd>
<kwd lng="es"><![CDATA[inhibidores enzima convertidora de angiotensina]]></kwd>
<kwd lng="es"><![CDATA[hipertensión.]]></kwd>
<kwd lng="en"><![CDATA[acute renal failure]]></kwd>
<kwd lng="en"><![CDATA[systemic sclerosis]]></kwd>
<kwd lng="en"><![CDATA[angiotensin converting enzyme inhibitors]]></kwd>
<kwd lng="en"><![CDATA[hypertension.]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Guillevin]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Bérezné]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Seror]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Teixeira]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Pourrat]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Mahr]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma renal crisis: a retrospective multicentre study on 91 patients and 427 controls]]></article-title>
<source><![CDATA[Rheumatology (Oxford)]]></source>
<year>2010</year>
<volume>51</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>460-7</page-range></nlm-citation>
</ref>
<ref id="B2">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mouthon]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Bérezné]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Bussone]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Noël]]></surname>
<given-names><![CDATA[L-H]]></given-names>
</name>
<name>
<surname><![CDATA[Villiger]]></surname>
<given-names><![CDATA[PM]]></given-names>
</name>
<name>
<surname><![CDATA[Guillevin]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma renal crisis: a rare but severe complication of systemic sclerosis]]></article-title>
<source><![CDATA[Clin Rev Allergy Immunol]]></source>
<year>2011</year>
<volume>40</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>84-91</page-range></nlm-citation>
</ref>
<ref id="B3">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Abbott]]></surname>
<given-names><![CDATA[KC]]></given-names>
</name>
<name>
<surname><![CDATA[Trespalacios]]></surname>
<given-names><![CDATA[FC]]></given-names>
</name>
<name>
<surname><![CDATA[Welch]]></surname>
<given-names><![CDATA[PG]]></given-names>
</name>
<name>
<surname><![CDATA[Agodoa]]></surname>
<given-names><![CDATA[LYC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma at end stage renal disease in the United States: patient characteristics and survival]]></article-title>
<source><![CDATA[J Nephrol]]></source>
<year>2002</year>
<volume>15</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>236-40</page-range></nlm-citation>
</ref>
<ref id="B4">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Penn]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Howie]]></surname>
<given-names><![CDATA[AJ]]></given-names>
</name>
<name>
<surname><![CDATA[Kingdon]]></surname>
<given-names><![CDATA[EJ]]></given-names>
</name>
<name>
<surname><![CDATA[Bunn]]></surname>
<given-names><![CDATA[CC]]></given-names>
</name>
<name>
<surname><![CDATA[Stratton]]></surname>
<given-names><![CDATA[RJ]]></given-names>
</name>
<name>
<surname><![CDATA[Black]]></surname>
<given-names><![CDATA[CM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma renal crisis: patient characteristics and long-term outcomes]]></article-title>
<source><![CDATA[QJM Int J Med]]></source>
<year>2007</year>
<volume>100</volume>
<numero>8</numero>
<issue>8</issue>
<page-range>485-94</page-range></nlm-citation>
</ref>
<ref id="B5">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Alenzi]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma renal crisis: Importance of knowing and differentiating in emergency unit (Internet)]]></article-title>
<source><![CDATA[Int J Clin Rheumtol]]></source>
<year>2019</year>
<volume>14</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>279</page-range></nlm-citation>
</ref>
<ref id="B6">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Trimarchi]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Calvo]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Malvar]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Alberton]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Lococo]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Greloni]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfermedades Glomerulares]]></article-title>
<source><![CDATA[Asociación Nef Buenos Aires (ANBA): El Edén del Hipocampo]]></source>
<year>2017</year>
<numero>1</numero>
<issue>1</issue>
<page-range>616-21</page-range></nlm-citation>
</ref>
<ref id="B7">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Steen]]></surname>
<given-names><![CDATA[VD]]></given-names>
</name>
<name>
<surname><![CDATA[Costantino]]></surname>
<given-names><![CDATA[JP]]></given-names>
</name>
<name>
<surname><![CDATA[Shapiro]]></surname>
<given-names><![CDATA[AP]]></given-names>
</name>
<name>
<surname><![CDATA[Medsger]]></surname>
<given-names><![CDATA[TA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Outcome of renal crisis in systemic sclerosis: relation to availability of angiotensin converting enzyme (ACE) inhibitors]]></article-title>
<source><![CDATA[Ann Intern Med]]></source>
<year>1990</year>
<volume>113</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>352-7</page-range></nlm-citation>
</ref>
<ref id="B8">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cannon]]></surname>
<given-names><![CDATA[PJ]]></given-names>
</name>
<name>
<surname><![CDATA[Hassar]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Case]]></surname>
<given-names><![CDATA[DB]]></given-names>
</name>
<name>
<surname><![CDATA[Casarella]]></surname>
<given-names><![CDATA[WJ]]></given-names>
</name>
<name>
<surname><![CDATA[Sommers]]></surname>
<given-names><![CDATA[SC]]></given-names>
</name>
<name>
<surname><![CDATA[LeRoy]]></surname>
<given-names><![CDATA[EC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The relationship of hypertension and renal failure in scleroderma (progressive systemic sclerosis) to structural and functional abnormalities of the renal cortical circulation]]></article-title>
<source><![CDATA[Medicine (Baltimore)]]></source>
<year>1974</year>
<volume>53</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>1-46</page-range></nlm-citation>
</ref>
<ref id="B9">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Donohoe]]></surname>
<given-names><![CDATA[JF]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma and the kidney]]></article-title>
<source><![CDATA[Kidney Int]]></source>
<year>1992</year>
<volume>41</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>462-77</page-range></nlm-citation>
</ref>
<ref id="B10">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Steen]]></surname>
<given-names><![CDATA[VD]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Scleroderma renal crisis]]></article-title>
<source><![CDATA[Rheum Dis Clin North Am]]></source>
<year>2003</year>
<volume>29</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>315-33</page-range></nlm-citation>
</ref>
<ref id="B11">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Woodworth]]></surname>
<given-names><![CDATA[TG]]></given-names>
</name>
<name>
<surname><![CDATA[Furst]]></surname>
<given-names><![CDATA[DE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Timely renal transplantation for scleroderma end-stage kidney disease patients can improve outcomes and quality of life]]></article-title>
<source><![CDATA[Ann Transl Med]]></source>
<year>2019</year>
<volume>7</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>60</page-range></nlm-citation>
</ref>
<ref id="B12">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jara]]></surname>
<given-names><![CDATA[LJ]]></given-names>
</name>
<name>
<surname><![CDATA[Barrera]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Afección renal en la esclerosis sistémica]]></article-title>
<source><![CDATA[Reumatol Clin]]></source>
<year>2006</year>
<volume>2</volume>
<page-range>S20-3</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
